Collaborative Stage Data Set - Revised 11/11/2010 FINAL

LymphomaOcularAdnexa

CS Extension

Note 1: Ocular adnexal lymphomas (OAL) originate in conjunctiva, eyelids, lacrimal gland, lacrimal drainage apparatus, and other orbital tissues surrounding the eye. This schema should not be used for secondary lymphomatous involvement of ocular adnexa or for intraocular lymphomas.
Note 2: Preseptal eyelid involvement includes infiltration of the outer three layers of the eyelid:skin, subcutaneous connective tissue, and orbicularis oculi muscle.
Note 3: The orbit is the bony cavity containing the eye, lacrimal gland, lacrimal sac, nasolacrimal duct, extraocular muscles, fat. arteries, veins, and nerves, but no lymphatics.
Note 4: Unknown extension is coded 989. Code 999, used for lymphoma staging in CS Version1, is an obsolete code for this schema.

Code	Description	TNM 7 Map	TNM 6 Map	SS77 Map	SS2000 Map
100	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of a single lymph node region Stage I	ERROR	*	L	L
105	Lymphoma involving bulbar conjunctiva only WITHOUT orbital involvement Stated as T1a with no other information on extension	T1a	**	L	L
110	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Localized involvement of a single extralymphatic organ/site in the absence of any lymph node involvement Multifocal involvement of one extralymphatic organ/site Stage IE	ERROR	*	L	L
115	Palpebral conjunctiva WITHOUT orbital involvement: With or without involvement of the fornix With or without involvement of the caruncle Stated as T1b with no other information on extension	T1b	**	L	L
120	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of spleen only Stage IS	ERROR	*	RNOS	RNOS
125	Extensive conjunctival involvement Stated as T1c with no other information on extension	T1c	**	L	L
150	Conjunctiva alone WITHOUT orbital involvement, Conjunctiva, NOS Stated as T1[NOS] with no other information on extension	T1NOS	**	L	L
200	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of two or more lymph node regions on the SAME side of the diaphragm Stage II	ERROR	*	RNOS	RNOS
210	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Localized involvement of a single extralymphatic organ/site WITH involvement of its regional lymph node(s) or WITH or without involvement of other lymph node(s) on the SAME site of the diaphragm Direct extension to adjacent organs or tissues Stage IIE	ERROR	*	RNOS	RNOS
220	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of spleen PLUS lymph node(s) BELOW the diaphragm Stage IIS	ERROR	*	RNOS	RNOS
230	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of spleen PLUS involvement of a single extralymphatic organ/site BELOW the diaphragm WITH/WITHOUT involvement of lymph node(s) BELOW the diaphragm Stage IIES	ERROR	*	RNOS	RNOS
300	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of lymph node regions on BOTH sides of the diaphragm Stage III	ERROR	*	D	D
305	Anterior orbit With or without conjunctival involvement Stated as T2a with no other information on extension	T2a	**	L	L
310	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of an extralymphatic organ/site PLUS involvement of lymph node(s) on the OPPOSITE side of the diaphragm Stage IIIE	ERROR	*	D	D
315	Anterior orbit WITH lacrimal involvement: With or without conjunctival involvement Stated as T2b with no other information on extension	T2b	**	L	L
320	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Involvement of the spleen PLUS lymph node(s) ABOVE the diaphragm Involvement of spleen PLUS lymph nodes on both sides of the diaphragm Stage IIIS	ERROR	*	D	D
325	Posterior orbit: With or without conjunctival involvement With or without anterior involvement With or without extraocular muscle involvement Stated as T2c with no other information on extension	T2c	**	L	L
330	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 (310 + 320) OR Involvement of the spleen PLUS a single extralymphatic site ABOVE the diaphragm WITH/WITHOUT involvement of lymph node(s) Involvement of the spleen PLUS involvement of lymph node region(s) ABOVE the diaphragm PLUS involvement of a single extralymphatic organ/site on either side of the diaphragm Stage IIIES	ERROR	*	D	D
335	Nasolacrimal drainage system: With or without conjunctival involvement Without nasopharynx involvement Stated as T2d with no other information on extension	T2d	**	L	L
350	Orbital involvement: With or without conjunctival involvement Stated as T2 [NOS] with no other information on extension	T2NOS	**	L	L
500	Pre-septal eyelid involvement: With or without orbital involvement With or without conjunctival involvement Stated as T3 with no other information on extension	T3	**	L	L
700	Nasopharynx Stated as T4a with no other information on extension	T4a	**	D	D
710	Osseous involvement including periosteum Stated as T4b with no other information on extension	T4b	**	D	D
720	Maxillofacial, ethmoidal, and/or frontal sinuses Stated as T4c with no other information on extension	T4c	**	D	D
730	Intracranial spread Stated as T4d with no other information on extension	T4d	**	D	D
750	Extension beyond orbit to adjacent structures, NOS Stated as T4 [NOS] with no other information on extension	T4NOS	**	D	D
800	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Diffuse or disseminated (multifocal) involvement of ONE OR MORE extralymphatic organ(s)/site(s) WITH OR WITHOUT associated lymph node involvement Multifocal involvement of MORE THAN ONE extralymphatic organ/site Involvement of isolated extralymphatic organ in absence of involvement of adjacent lymph nodes, but in conjunction with disease in distant sites Metastasis/involvement: Bone marrow Liver Nodular involvement of lung(s) Stage IV	ERROR	*	D	D
805	Further contiguous extension beyond any structure in codes 700 - 730	T4NOS	**	D	D
950	No evidence of primary tumor	T0	**	U	U
989	Unknown; extension not stated Primary tumor cannot be assessed Not documented in patient record	TX	**	U	U
999	OBSOLETE DATA RETAINED V0200 New schema for site/histology V0200 Unknown extension Primary tumor cannot be assessed Not documented in patient record	ERROR	*	U	U

* Stage grouping for AJCC 6 staging of ocular adnexal lymphoma for cases using obsolete codes is derived directly from the CS Extension code as shown in the AJCC TNM 6 Stage CSv1 table. A or B classification is appended to Stage I-IV based on coding of CS Site-Specific Factor 2, Systemic Symptoms at Diagnosis.
** Stage grouping for AJCC 6 staging of ocular adnexal lymphoma is derived from a combination of CS Extension, CS Lymph Nodes, and CS Mets at DX codes as shown in the AJCC TNM 6 Stage table. A or B classification is appended to Stage I-IV based on coding of CS Site-Specific Factor 2, Systemic Symptoms at Diagnosis.

List of Schemas LymphomaOcularAdnexa Schema Index